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Phenylbutyrate, a branched‐chain amino acid keto dehydrogenase activator, promotes branched‐chain amino acid metabolism and induces muscle catabolism in C2C12 cellsCrossland, Hannah ; Smith, Kenneth ; Idris, Iskandar ; Phillips, Bethan E. ; Atherton, Philip J ; Wilkinson, Daniel JExperimental physiology, 2021-03, Vol.106 (3), p.585-592 [Periódico revisado por pares]England: John Wiley & Sons, IncTexto completo disponível |
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Branched‐chain keto‐acid dehydrogenase kinase regulates vascular permeability and angiogenesis to facilitate tumor metastasis in renal cell carcinomaYang, Kunao ; Xu, Chunlan ; Sun, Huimin ; Xuan, Zuodong ; Liu, Yankuo ; Li, Jinxin ; Bai, Yang ; Zheng, Zeyuan ; Zhao, Yue ; Shi, Zhiyuan ; Zheng, Jianzhong ; Shao, ChenCancer science, 2023-11, Vol.114 (11), p.4270-4285 [Periódico revisado por pares]Tokyo: John Wiley & Sons, IncTexto completo disponível |
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Mechanisms of activation of muscle branched-chain alpha-keto acid dehydrogenase during exercise in manvan Hall, G ; MacLean, D A ; Saltin, B ; Wagenmakers, A JThe Journal of physiology, 1996-08, Vol.494 (Pt 3), p.899-905 [Periódico revisado por pares]England: The Physiological SocietyTexto completo disponível |
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Downregulation of extramitochondrial BCKDH and its uncoupling from AMP deaminase in type 2 diabetic OLETF rat heartsOgawa, Toshifumi ; Kouzu, Hidemichi ; Osanami, Arata ; Tatekoshi, Yuki ; Sato, Tatsuya ; Kuno, Atsushi ; Fujita, Yugo ; Ino, Shoya ; Shimizu, Masaki ; Toda, Yuki ; Ohwada, Wataru ; Yano, Toshiyuki ; Tanno, Masaya ; Miki, Takayuki ; Miura, TetsujiPhysiological reports, 2023-02, Vol.11 (4), p.e15608-n/a [Periódico revisado por pares]United States: John Wiley & Sons, IncTexto completo disponível |
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Material Type: Artigo
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Conformational stability and thermodynamic characterization of the lipoic acid bearing domain of human mitochondrial branched chain α‐ketoacid dehydrogenaseNaik, Mandar T. ; Huang, Tai‐HuangProtein science, 2004-09, Vol.13 (9), p.2483-2492 [Periódico revisado por pares]Bristol: Cold Spring Harbor Laboratory PressTexto completo disponível |
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Diabetes and branched‐chain amino acids: What is the link?Bloomgarden, ZacharyJournal of diabetes, 2018-05, Vol.10 (5), p.350-352 [Periódico revisado por pares]Melbourne: Wiley Publishing Asia Pty LtdTexto completo disponível |
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Effects of ketoisocaproic acid and inflammation on glucose transport in muscle cellsMann, Gagandeep ; Adegoke, Olasunkanmi A. J.Physiological reports, 2021-01, Vol.9 (1), p.e14673-n/a [Periódico revisado por pares]United States: John Wiley & Sons, IncTexto completo disponível |
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Molecular basis of various forms of maple syrup urine disease in Chilean patientsCampanholi, Diana Ruffato Resende ; Margutti, Ana Vitoria Barban ; Silva, Wilson A. ; Garcia, Daniel F. ; Molfetta, Greice A. ; Marques, Adriana A. ; Schwartz, Ida Vanessa Döederlein ; Cornejo, V. ; Hamilton, Valerie ; Castro, Gabriela ; Sperb‐Ludwig, Fernanda ; Borges, Ester S. ; Camelo, José S.Molecular genetics & genomic medicine, 2021-05, Vol.9 (5), p.e1616-n/a [Periódico revisado por pares]United States: John Wiley & Sons, IncTexto completo disponível |
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Biochemical characterization of patients with dihydrolipoamide dehydrogenase deficiencyWongkittichote, Parith ; Cuddapah, Sanmati R. ; Master, Stephen R. ; Grange, Dorothy K. ; Dietzen, Dennis ; Roper, Stephen M. ; Ganetzky, Rebecca D.JIMD reports, 2023-09, Vol.64 (5), p.367-374 [Periódico revisado por pares]Hoboken: John Wiley & Sons, IncTexto completo disponível |
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Identification of novel mutations in BCKDHB and DBT genes in Vietnamese patients with maple sirup urine diseaseNguyen, Thi T. N. ; Vu, Chi D. ; Nguyen, Ngoc L. ; Nguyen, Thi T. H. ; Nguyen, Ngoc K. ; Nguyen, Huy H.Molecular genetics & genomic medicine, 2020-08, Vol.8 (8), p.e1337-n/a [Periódico revisado por pares]United States: John Wiley & Sons, IncTexto completo disponível |