NEDD4-family E3 ligase dysfunction due to PKHD1/Pkhd1 defects suggests a mechanistic model for ARPKD pathobiology
Jun-ya Kaimori Cheng-Chao Lin; Patricia Outeda; Miguel A Garcia-Gonzalez; Luis F Menezes; Erum A Hartung; Ao Li; Guanqing Wu; Hideaki Fujita; Yasunori Sato; Yasuni Nakanuma; Satoko Yamamoto; Naotsugu Ichimaru; Shiro Takahara; Yoshitaka Isaka; Terry Watnick; Luiz F Onuchic; Lisa M Guay-Woodford; Gregory G Germino
Scientific Reports v. 7, n. 7733, p. 1-16, 2017United Kingdom 2017
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