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Material Type: Artigo
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Long-term outcomes of 176 patients with X-linked hyper-IgM syndrome treated with or without hematopoietic cell transplantationMaria Teresa de la Morena David Leonard; Troy R Torgerson; Otavio Cabral Marques; Mary Anne Slatter; Asghar Aghamohammadi; Sharat Chandra; Luis Murguia Favela; Francisco A Bonilla; Maria Kanariou; Rongras Damrongwatanasuk; Caroline Y Kuo; Christopher C Dvorak; Isabelle Meyts; Karin Chen; Lisa Kobrynski; Neena Kapoor; Darko Richter; Daniela DiGiovanni; Fatima Dhalla; Evangelia Farmaki; Carsten Speckmann; Teresa Español; Anna YU Shcherbina; Imelda Celine Guerra Hanson; Jiri Litzman; John M Routes; Melanie Wong; Ramsay Fuleihan; Suranjith L Seneviratne; Trudy N Small; Ales Janda; Liliana Bezrodnik; Reinhard Seger; Andrea Gomez Raccio; John David M Edgar; Janet Chou; Jordan Keith Abbott; Joris van Montfrans; Luis Ignacio González Granado; Nancy Bunin; Necil Kutukculer; Paul Gray; Gisela Seminario; Srdjan Pasic; Victor Aquino; Christian Wysocki; Hassan Abolhassani; Morna Dorsey; Charlotte Cunningham Rundles; Alan Paul Knutsen; John William Sleasman; Beatriz Tavares Costa Carvalho; Antonio Condino-Neto; Eyal Grunebaum; Helen Chapel; Hans Dieter Ochs; Alexandra Hult Filipovich; Mort Cowan; Andrew Gennery; Andrew James Cant; Luigi D Notarangelo; Chaim M RoifmanJournal of Allergy and Clinical Immunology v. 139, n. 4, p. 1282-1292, 2017Philadelphia 2017Item não circula. Consulte sua biblioteca.(Acessar) |
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Material Type: Artigo
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X-linked agammaglobulinemia (XLA) phenotype, diagnosis, and therapeutic challenges around the worldZeinab A. El-Sayed Irina Abramova; Juan Carlos Aldave; Waleed Al-Herz; Liliana Bezrodnik; Rachida Boukari; Ahmed Aziz Bousfilha; Caterina Cancrini; Ghassan Dbaibo; Beata Derfalvi; Figen Dogu; J. Davi M Edgar; Brian Eley; Rasha Hasan El-Owaidy; Sara Elva Espinosa-Padilla; Nermeen Galal; Filomeen Haerynck; Rima Hanna-Wakim; Elham Hossny; Aydan Ikinciogullari; Ebtihal Kamal; Hirokaku Kanegane; Nadia Kechout; Yu Lung Lau; Tomohiro Morio; Viviana Moschese; João Farela Neves; Monia Quederni; Roberto Paganelli; Kenneth Paris; Claudia Pignata; Alessandro Plebani; Farah Naz Qamar; Sonia Qureshi; Nita Radhakrishnan; Nima Rezaei; Nelson Rosario; John Routes; Berta Sanchez; Anna Sediva; Mikko Risto Juhana Seppanen; Edith Gonzalez Serrano; Anna Shcherbina; Surjit Singh; Sangeetha Siniah; Guiseppe Spadaro; Mimi Tang; Ana Maria Vinet; Alla Volokha; Kathleen E Sullivan; Antonio Condino NetoWorld Allergy Organization Journal Amsterdam v. 12, Art. 100018, 9 p., 2019Amsterdam 2019Item não circula. Consulte sua biblioteca.(Acessar) |
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Material Type: Artigo
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Autoantibodies neutralizing type I IFNs are present in ~4% of uninfected individuals over 70 years old and account for ~20% of COVID-19 deathsPaul Bastard Adrian Gervais; Tom Le Voyer; Jérémie Rosain; Quentin Philippot; Jérémy Manry; Eleftherios Michailidis; Hans-Heinrich Hoffmann; Shohei Eto; Marina Garcia-Prat; Lucy Bizien; Alba Parra-Martínez; Rui Yang; Haljasmägi Liis; Mélanie Migaud; Karita Särekannu; Julia Maslovskaja; Nicolas de Prost; Yacine Tandjaoui-Lambiotte; Charles-Edouard Luyt; Blanca Amador-Borrero; Gaudet Alexandre; Julien Poissy; Pascal Morel; Pascale Richard; Fabrice Cognasse; Jesus Troya; Sophie Trouillet-Assant; Alexandre Belot; Kahina Saker; Pierre Garçon; Jacques G Rivière; Jean-Christophe Lagier; Stéphanie Gentile; Lindsey B Rosen; Elana Shaw; Tomohiro Morio; Junko Tanaka; David Dalmau; Pierre-Louis Tharaux; Damien Sene; Alain Stepanian; Bruno Megarbane; Vasiliki Triantafyllia; Arnaud Fekkar; James R Heath; José Luis Franco; Juan-Manuel Anaya; Jordi Solé-Violán; Luisa Imberti; Andrea Biondi; Paolo Bonfanti; Riccardo Castagnoli; Ottavia M Delmonte; Yu Zhang; Andrew L Snow; Steven M Holland; Catherine M Biggs; Marcela Moncada-Vélez; Andrés Augusto Arias; Lazaro Lorenzo; Soraya Boucherit; Boubacar Coulibaly; Dany Anglicheau; Anna M Planas; Filomeen Haerynck; Sotirija Duvlis; Robert L Nussbaum; Tayfun Ozcelik; Sevgi Keles; Ahmed A Bousfiha; Jalila ElBakkouri; Carolina Ramirez-Santana; Stéphane Paul; Qiang Pan-Hammarström; Lennart Hammarström; Annabelle Dupont; Alina Kurolap; Christine N Metz; Alessandro Aiuti; Giorgio Casari; Vito Lampasona; Fabio Ciceri; Lucila A Barreiros; Elena Dominguez-Garrido; Mateus Vidigal; Mayana Zatz; Diederik van de Beek; Sabina Sahanic; Ivan Tancevski; Yurii Stepanovskyy; Oksana Boyarchuk; Yoko Nukui; Miyuki Tsumura; Loreto Vidaur; Stuart G Tangye; Sonia Burrel; Darragh Duffy; Lluis Quintana-Murci; Adam Klocperk; Nelli Y Kann; Anna Shcherbina; Yu-Lung Lau; Daniel Leung; Matthieu Coulongeat; Julien Marlet; Rutger Koning; Luis Felipe Reyes; Angélique Chauvineau-Grenier; Fabienne Vene; Guillaume Monneret; Michel C Nussenzweig; Romain Arrestier; Idris Boudhabhay; Hagit Baris-Feldman; David Hagin; Joost Wauters; Isabelle Meyts; Adam H Dyer; Sean P Kennelly; Nollaig M Bourke; Rabih Halwani; Narjes Saheb Sharif-Askari; Karim Dorgham; Jérome Sallette; Souad Mehlal Sedkaoui; Suzan AlKhater; Raúl Rigo-Bonnin; Francisco Morandeira; Lucie Roussel; Donald C Vinh; Sisse Rye Ostrowski; Antonio Condino Neto; Carolina Prando; Anastasiia Bondarenko; András N Spaan; Laurent Gilardin; Jacques Fellay; Stanislas Lyonnet; Kaya Bilguvar; Richard P Lifton; Shrikant Mane; Mark S Anderson; Bertrand Boisson; Vivien Béziat; Shen-Ying Zhang; Evangelos Andreakos; Olivier Hermine; Aurora Pujol; Pärt Peterson; Trine Mogensen; Lee H Rowen; James Mond; Stéphanie Debette; Xavier de Lamballerie; Xavier Duval; France Mentré; Marie Zins; Pere Soler-Palacin; Roger Colobran; Guy Gorochov; Xavier Solanich; Sophie Susen; Javier Martinez-Picado; Didier Raoult; Marc Vasse; Peter K Gregersen; Lorenzo Piemonti; Carlos Rodríguez-Gallego; Luigi D Notarangelo; Helen C Su; Kai Kisand; Satoshi Okada; Anne Puel; Emmanuelle Jouanguy; Charles M Rice; Pierre Tiberghien; Qian Zhang; Aurélie Cobat; Laurent Abel; Jean-Laurent Casanova; HGID Lab; COVID Clinicians; COVID-STORM Clinicians; NIAID Immune Response to COVID Group; NH-COVAIR Study Group; Danish CHGE; Danish Blood Donor Study; St. James’s Hospital SARS CoV2 Interest group; French COVID Cohort Study Group; Imagine COVID-Group; The Milieu Intérieur Consortium; CoV-Contact Cohort; Amsterdam UMC Covid-19 Biobank Investigators; COVID Human Genetic Effort; CONSTANCES cohort; 3C-Dijon Study; Cerba HealthCare; Etablissement du Sang study groupScience Immunology Washington v. 6, n. 62, p. 1-30, 2021Washington 2021Item não circula. Consulte sua biblioteca.(Acessar) |
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Material Type: Artigo
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Long-Sought Redox Isomerization of the Europium(III/II) Complex Achieved by Molecular Reorientation at the InterfaceShokurov, Alexander V ; Kutsybala, Daria S ; Martynov, Alexander G ; Bakirov, Artem V ; Shcherbina, Maxim A ; Chvalun, Sergei N ; Gorbunova, Yulia G ; Tsivadze, Aslan Yu ; Zaytseva, Anna V ; Novikov, Dmitri ; Arslanov, Vladimir V ; Selektor, Sofiya LLangmuir, 2020-02, Vol.36 (6), p.1423-1429 [Periódico revisado por pares]United States: American Chemical SocietyTexto completo disponível |
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Material Type: Artigo
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Modification of Epoxy Coatings with Fluorocontaining Organosilicon CopolymersKrutskikh, Dmitriy V. ; Shapagin, Aleksey V. ; Plyusnina, Irina O. ; Budylin, Nikita Yu ; Shcherbina, Anna A. ; Soldatov, Mikhail A.Polymers, 2024-06, Vol.16 (11), p.1571 [Periódico revisado por pares]Basel: MDPI AGTexto completo disponível |
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Material Type: Artigo
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Human genetic and immunological determinants of critical COVID-19 pneumoniaZhang, Qian ; Bastard, Paul ; Cobat, Aurélie ; Casanova, Jean-LaurentNature (London), 2022-03, Vol.603 (7902), p.587-598 [Periódico revisado por pares]England: Nature Publishing GroupTexto completo disponível |
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Material Type: Artigo
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Studying severe long COVID to understand post-infectious disorders beyond COVID-19Brodin, Petter ; Casari, Giorgio ; Townsend, Liam ; O'Farrelly, Cliona ; Tancevski, Ivan ; Löffler-Ragg, Judith ; Mogensen, Trine H ; Casanova, Jean LaurentNature medicine, 2022-05, Vol.28 (5), p.879-882 [Periódico revisado por pares]United States: Nature Publishing GroupTexto completo disponível |
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Material Type: Artigo
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A global effort to dissect the human genetic basis of resistance to SARS-CoV-2 infectionAndreakos, Evangelos ; Abel, Laurent ; Vinh, Donald C ; Kaja, Elżbieta ; Drolet, Beth A ; Zhang, Qian ; O'Farrelly, Cliona ; Novelli, Giuseppe ; Rodríguez-Gallego, Carlos ; Haerynck, Filomeen ; Prando, Carolina ; Pujol, Aurora ; Su, Helen C ; Casanova, Jean-Laurent ; Spaan, András NNature immunology, 2022-02, Vol.23 (2), p.159-164 [Periódico revisado por pares]United States: Nature Publishing GroupTexto completo disponível |
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Material Type: Artigo
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Characterization of a Novel Pathogenic PLCG2 Variant Leading to APLAID Syndrome Responsive to a TNF inhibitorYang, Zhaohui ; Tao, Panfeng ; Han, Xu ; Kozlova, Anna ; He, Tingyan ; Volchkov, Egor ; Nesterenko, Zoya ; Pershin, Dmitryi ; Raykina, Elena ; Fatkhudinov, Timur ; Korobeynikova, Anastasia ; Aksentijevich, Ivona ; Yang, Jun ; Shcherbina, Anna ; Zhou, Qing ; Yu, XiaominArthritis & rheumatology (Hoboken, N.J.), 2024-07 [Periódico revisado por pares]Texto completo disponível |
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Material Type: Artigo
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Structures and Stability of Complexes of E(C6F5)3 (E = B, Al, Ga, In) with AcetonitrileShcherbina, Nadezhda A. ; Pomogaeva, Anna V. ; Lisovenko, Anna S. ; Kazakov, Igor V. ; Gugin, Nikita Yu ; Khoroshilova, Olesya V. ; Kondrat'ev, Yuri V. ; Timoshkin, Alexey Y.Zeitschrift für anorganische und allgemeine Chemie (1950), 2020-07, Vol.646 (13), p.873-881 [Periódico revisado por pares]Weinheim: Wiley Subscription Services, IncTexto completo disponível |